Login
Search
Search
0 Dates
2026
2025
2024
2023
2022
2021
2020
2019
2018
0 Events
CPC 2018
CPC 2019
Curso de Atualização em Medicina Cardiovascular 2019
Reunião Anual Conjunta dos Grupos de Estudo de Cirurgia Cardíaca, Doenças Valvulares e Ecocardiografia da SPC
CPC 2020
CPC 2021
CPC 2022
CPC 2023
CPC 2024
CPC 2025
CPC 2026
0 Topics
A. Basics
B. Imaging
C. Arrhythmias and Device Therapy
D. Heart Failure
E. Coronary Artery Disease, Acute Coronary Syndromes, Acute Cardiac Care
F. Valvular, Myocardial, Pericardial, Pulmonary, Congenital Heart Disease
G. Aortic Disease, Peripheral Vascular Disease, Stroke
H. Interventional Cardiology and Cardiovascular Surgery
I. Hypertension
J. Preventive Cardiology
K. Cardiovascular Disease In Special Populations
L. Cardiovascular Pharmacology
M. Cardiovascular Nursing
N. E-Cardiology / Digital Health, Public Health, Health Economics, Research Methodology
O. Basic Science
P. Other
0 Themes
01. History of Cardiology
02. Clinical Skills
03. Imaging
04. Arrhythmias, General
05. Atrial Fibrillation
06. Supraventricular Tachycardia (non-AF)
07. Syncope and Bradycardia
08. Ventricular Arrhythmias and Sudden Cardiac Death (SCD)
09. Device Therapy
10. Chronic Heart Failure
11. Acute Heart Failure
12. Coronary Artery Disease (Chronic)
13. Acute Coronary Syndromes
14. Acute Cardiac Care
15. Valvular Heart Disease
16. Infective Endocarditis
17. Myocardial Disease
18. Pericardial Disease
19. Tumors of the Heart
20. Congenital Heart Disease and Pediatric Cardiology
21. Pulmonary Circulation, Pulmonary Embolism, Right Heart Failure
22. Aortic Disease
23. Peripheral Vascular and Cerebrovascular Disease
24. Stroke
25. Interventional Cardiology
26. Cardiovascular Surgery
27. Hypertension
28. Risk Factors and Prevention
29. Rehabilitation and Sports Cardiology
30. Cardiovascular Disease in Special Populations
31. Pharmacology and Pharmacotherapy
32. Cardiovascular Nursing
33. e-Cardiology / Digital Health
34. Public Health and Health Economics
35. Research Methodology
36. Basic Science
37. Miscellanea
0 Resources
Abstract
Slides
Vídeo
Report
CLEAR FILTERS
Unveiling the True Burden of Hospitalizations in Pulmonary Arterial Hypertension: A Comprehensive Follow-up Analysis
Session:
Sessão de Posters 57 - Hipertensão arterial pulmonar: estratificação de risco, hemodinâmica e prognóstico
Speaker:
Liliana Brochado
Congress:
CPC 2026
Topic:
F. Valvular, Myocardial, Pericardial, Pulmonary, Congenital Heart Disease
Theme:
21. Pulmonary Circulation, Pulmonary Embolism, Right Heart Failure
Subtheme:
21.2 Pulmonary Circulation, Pulmonary Embolism, Right Heart Failure – Epidemiology, Prognosis, Outcome
Session Type:
Posters Eletrónicos
FP Number:
---
Authors:
Liliana Brochado; João Mirinha Luz; Filipa Ferreira; Paula Fazendas; Sofia Alegria; Ana Claudia Vieira; Bárbara Ferreira; Débora Repolho; Hélder Pereira
Abstract
<p style="text-align:justify"><span style="font-size:medium"><span style="font-family:Calibri,sans-serif"><span style="color:#000000"><strong>Background:</strong> Hospitalizations are frequent in pulmonary arterial hypertension (PAH) and carry major prognostic implications. Yet, most studies focus only on the first admission, potentially underestimating the cumulative clinical burden and its long-term impact.</span></span></span></p> <p style="text-align:justify"> </p> <p style="text-align:justify"><span style="font-size:medium"><span style="font-family:Calibri,sans-serif"><span style="color:#000000"><strong>Purpose:</strong> To comprehensively characterize all hospitalizations during long-term follow-up in a real-world PAH cohort, differentiating PAH-related from unrelated causes and assessing their prognostic significance.</span></span></span></p> <p style="text-align:justify"> </p> <p style="text-align:justify"><span style="font-size:medium"><span style="font-family:Calibri,sans-serif"><span style="color:#000000"><strong>Methods:</strong> We retrospectively analysed all consecutive patients with confirmed PAH followed at a tertiary Pulmonary Hypertension Unit. All hospital admissions during follow-up were systematically reviewed and classified as PAH-related or unrelated. Hospitalizations for maternal delivery were excluded. Baseline characteristics, aetiology, and survival data were collected. Mean follow-up was 8.2 ± 5.9 years.</span></span></span></p> <p style="text-align:justify"> </p> <p style="text-align:justify"><span style="font-size:medium"><span style="font-family:Calibri,sans-serif"><span style="color:#000000"><strong>Results:</strong> Eighty-two patients were included, most were female (69.5%). The predominant aetiologies were congenital heart disease (32.9%), idiopathic PAH (20.7%), connective tissue disease (17,1%), and HIV-associated PAH (14.6%). </span></span></span></p> <p style="text-align:justify"><span style="font-size:medium"><span style="font-family:Calibri,sans-serif"><span style="color:#000000">During follow-up, 85.4% of patients were hospitalized at least once and 80% had ≥2 admissions. PAH-related hospitalizations occurred in 70.7% of patients, mainly for acute right heart failure (63.8%), therapy escalation (11.8%), right heart catheterization (9.9%), initiation of intravenous therapy (8.7%), or central line procedures (5.8%).<br /> PAH-unrelated hospitalizations affected 45.1% of patients, driven by respiratory failure (30.4%), non–line-related infections (19.1%), pneumonia (17.1%), surgical procedures (12.3%), and gastrointestinal disorders (12.3%).</span></span></span></p> <p style="text-align:justify"><span style="font-size:medium"><span style="font-family:Calibri,sans-serif"><span style="color:#000000">Overall mortality reached 40.2%. The coexistence of an acute heart failure admission and any PAH-unrelated hospitalization independently predicted reduced 5-year survival (HR 1.6; 95% CI 1.2–2.9; p = 0.01).</span></span></span></p> <p style="text-align:justify"> </p> <p style="text-align:justify"><span style="font-size:medium"><span style="font-family:Calibri,sans-serif"><span style="color:#000000"><strong>Conclusions:</strong> Recurrent hospitalizations are almost universal in PAH, encompassing both cardiac and non-cardiac causes. PAH-unrelated admissions represent a major and often overlooked component of disease burden. Their occurrence, particularly when combined with cardiac decompensation, is associated with worse long-term survival. These findings highlight the need for an integrated, multidisciplinary strategy aimed at preventing both PAH-related and unrelated hospitalizations to improve prognosis and quality of life in this vulnerable population.</span></span></span></p>
Slides
Our mission: To reduce the burden of cardiovascular disease
Visit our site